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KMID : 0811820070110010118
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Journal of Korean Society of Pediatric Nephrology
2007 Volume.11 No. 1 p.118 ~ p.125
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A Case of Wegener’s Granulomatosis with Multi-organ Involvement in Childhood
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Lee Hyun-Kyung
Cho Hee-Yeon
Ha Il-Soo
Cheong Hae-Il
Choi Yong
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Abstract
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Wegener’’s granulomatosis(WG) is a necrotizing granulomatous small vessel vasculitis with a clinical predilection for involvement of the upper airways, lungs and kidneys. The disease usually manifests in adults between 25 and 50 years of age, but it can also rarely occur-in childhood with some features different from those of adults. WG may be easily overlooked in young patients by misinterpretion of the symptoms as caused by an infectious disease of the respiratory tract. Delayed diagnosis and treatment of the disease may cause more rapid progression of the glomerulonephritis to end stage renal disease. We report a boy who was diagnosed with WG with involvement of multiple organs at 13 years of age.
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KEYWORD
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Childhood, Wegener’s granulomatosis, Multi-organ involvement
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